Prenatal Diagnosis and Management of a Huge Infratentorial/Supratentorial Multiloculated Arachnoid Cystic Malformation in an Infant

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A 23-year-old woman had a normal fetal ultrasound at 16 weeks’ gestation. A second ultrasound at 25 weeks revealed a cystic brain malformation in the fetus. A fetal magnetic resonance image (MRI) at 28 weeks showed the presence of a huge infratentorial/supratentorial multiloculated arachnoid cystic malformation and hydrocephalus (A) . Although the prognosis was highly uncertain, the possibility of blindness, endocrine abnormalities, and severe developmental delay was discussed with the family. At 38 weeks, an infant boy was delivered via elective cesarian section with Apgar scores of 8 and 9 at 1 and 5 minutes, respectively. Other than macrocephaly with full fontanelles, the physical examination was normal and without evidence of diabetes insipidus. A postdelivery MRI found the cystic malf…